亚洲中文字幕特级毛片-亚洲制服丝袜中文字幕-亚洲制服丝袜在线观看-亚洲制服欧美自拍另类-免费一级黄色-免费一级国产生活片

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  人才招聘  關于我們  聯系我們
精品久久久久久成人av,aaa级久久久精品无码片,99在线精品免费视频九九视
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-TMEM70/AP Conjugated antibody (bs-12664R-AP)
訂購熱線:400-901-9800
訂購郵箱:sales@www.chomd.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@www.chomd.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-12664R-AP
英文名稱1 Rabbit Anti-TMEM70/AP Conjugated antibody
中文名稱 堿性磷酸酶(AP)標記的跨膜蛋白70抗體
別    名 FLJ20533; MC5DN2; mitochondrial; OTTHUMP00000226855; OTTHUMP00000226856; TMEM70; TMM70_HUMAN; Transmembrane protein 70; Transmembrane protein 70 mitochondrial; Transmembrane protein 70, mitochondrial.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  信號轉導  跨膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, )
產品應用 WB=1:50-200 IHC-P=1:50-200 IHC-F=1:50-200 ICC=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 21kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human TMEM70
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene likely encodes a mitochondrial membrane protein. The encoded protein may play a role in biogenesis of mitochondrial ATP synthase. Mutations in this gene have been associated with neonatal mitochondrial encephalocardiomyopathy due to ATP synthase deficiency. Alternatively spliced transcript variants have been described. [provided by RefSeq, Feb 2010]

Function:
Involved in biogenesis of mitochondrial ATP synthase.

Subcellular Location:
Mitochondrion inner membrane.

DISEASE:
Defects in TMEM70 are a cause of mitochondrial encephalocardiomyopathy neonatal due to ATP synthase deficiency (MT-ATPSD) [MIM:604273]; also known as ATPase deficiency. A mitochondrial disorder with heterogeneous clinical manifestations including dysmorphic features, psychomotor retardation, hypotonia, growth retardation, cardiomyopathy, enlarged liver, hypoplastic kidneys and elevated lactate levels in urine, plasma and cerebrospinal fluid.

Similarity:
Belongs to the TMEM70 family.

Database links:

Entrez Gene: 54968 Human

Entrez Gene: 70397 Mouse

Entrez Gene: 500384 Rat

Omim: 612418 Human

SwissProt: Q9BUB7 Human

SwissProt: Q921N7 Mouse

Unigene: 106650 Human

Unigene: 194225 Mouse

Unigene: 22296 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.www.chomd.com.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 欧美3区wwW抖阴视频大全| 久久精品亚洲一区二区三区浴池处 | 中文字幕丝袜诱惑操| 亚洲精品中文字幕乱码无线|亚 | 成人精品一区二区三区中文字幕_| 永久在线观看免费视频毛片一级一区二区三区 | 国产无遮挡又黄又大又爽网站| 中文字幕岛国高清四季偷拍| 天堂成人小说视频首页| 国产免费久久精品99久久,亚洲中文久久久久 | 亚洲m码 欧洲s码sss222岁 | 动漫无码无遮挡片子| 亚洲高清日本东京热视频观看 | 美女在线视频黄色抹胸直播| 免费国产男女色拍视频页面| 东北妇女精品一区| 亚洲 日韩 丝袜 熟女 变态| 国产午夜福利精品久久萌白麻酥酥| 亚洲尤物一区二区21页| 精品乱码一区内射人妻无码高清全集哪里可以看 | 人人妻人人爽凹凸视频| 99久久精品美女高潮喷水综合| 无码精品前田一区二区 - 99久久精| 国产无线乱码一区二三区大片 又粗又爽又猛又黄的视频 | 精品人妻一二三四区在交换视频 | 亚洲综合图色p14| 精品国产麻豆免费人成网站_第1集| 一边摸边吃奶边做爽动态图 | 无套内射在线无码播放,播放器| 国产午夜高清在线视频播放| 亚洲m码 欧洲s码sss222免费| 国产91在线亚洲美| 蜜芽tv深夜秘?入口| 一区二区三区911播放| 国内精品伊人久久久久网站_第38集| 亚洲精品美女在线观看播放 | 精品久久久久久亚洲精品网| 亚洲AV一卡二卡三卡不卡骚| 99热热久久这里只有精品68亚洲人人| 男人资源在线观看3d动漫无码专区| 在线观看视频vivo新出的nex|