亚洲中文字幕特级毛片-亚洲制服丝袜中文字幕-亚洲制服丝袜在线观看-亚洲制服欧美自拍另类-免费一级黄色-免费一级国产生活片

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  人才招聘  關于我們  聯系我們
亚洲国产成人高清在线观看,在线观看国产成人av天堂,欧美精品九九99久久在免费线
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-TMEM70/Gold Conjugated antibody (bs-12664R-Gold)
訂購熱線:400-901-9800
訂購郵箱:sales@www.chomd.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@www.chomd.com.cn
說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價
產品編號 bs-12664R-Gold
英文名稱1 Rabbit Anti-TMEM70/Gold Conjugated antibody
中文名稱 膠體金標記的跨膜蛋白70抗體
別    名 FLJ20533; MC5DN2; mitochondrial; OTTHUMP00000226855; OTTHUMP00000226856; TMEM70; TMM70_HUMAN; Transmembrane protein 70; Transmembrane protein 70 mitochondrial; Transmembrane protein 70, mitochondrial.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul(10nm  15nm  35nm
研究領域 腫瘤  細胞生物  信號轉導  跨膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, )
產品應用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 21kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human TMEM70
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產品介紹 background:
This gene likely encodes a mitochondrial membrane protein. The encoded protein may play a role in biogenesis of mitochondrial ATP synthase. Mutations in this gene have been associated with neonatal mitochondrial encephalocardiomyopathy due to ATP synthase deficiency. Alternatively spliced transcript variants have been described. [provided by RefSeq, Feb 2010]

Function:
Involved in biogenesis of mitochondrial ATP synthase.

Subcellular Location:
Mitochondrion inner membrane.

DISEASE:
Defects in TMEM70 are a cause of mitochondrial encephalocardiomyopathy neonatal due to ATP synthase deficiency (MT-ATPSD) [MIM:604273]; also known as ATPase deficiency. A mitochondrial disorder with heterogeneous clinical manifestations including dysmorphic features, psychomotor retardation, hypotonia, growth retardation, cardiomyopathy, enlarged liver, hypoplastic kidneys and elevated lactate levels in urine, plasma and cerebrospinal fluid.

Similarity:
Belongs to the TMEM70 family.

Database links:

Entrez Gene: 54968 Human

Entrez Gene: 70397 Mouse

Entrez Gene: 500384 Rat

Omim: 612418 Human

SwissProt: Q9BUB7 Human

SwissProt: Q921N7 Mouse

Unigene: 106650 Human

Unigene: 194225 Mouse

Unigene: 22296 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.www.chomd.com.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 乱亲女H秽乱长久久久笔趣阁| 国产又爽又黄又不遮挡视频,丰满又黄又爽少妇 | 国产精品外流一区二区| 国产成人精品视频2024| 伊人色婷婷综合在找 | Chinese国产在线视频重口猎奇| 亚洲永久在线观看地址最新| 男女拍拍拍免费视频网站| 丰满少妇被猛烈进入无码的| 亚洲精品无码成人片久久喷水入口 | a级毛片无码视频AAAA流出91| 亚洲不卡在线观看视频不卡在线| 久久久久亚洲AV无码专区网站,无码专区—VA亚洲V天堂 | 久久综合九色综合久99-日韩精品无码 | 日韩精品无码一区二区视频1000部| 国产乱码一区二区三区四区AV| 亚洲永久精品国产无损3D动漫 | 日本丰满人妻熟妇BBBBB| XXXX中文字幕视频在线观看免费 | 乱人伦中文视频在线观看免费版| A级黄色毛片视频怎么搜| 色婷婷国产传媒综合久久| zljzljzlj水多app| 人妻无码中文字幕按摩| caoporm视频网址| 乱亲女H秽乱长久久久文| 中日韩精品视频在线观看黑人| 两只大乳奶充满奶汁| 影音先锋Av资源x88AV | 99精品国产在热久久无毒不卡起碰2022国产 | 亚洲国产成人久久三区,国产亚洲欧美精 | 亚洲爆乳少妇无码激情小说| 国产精品外流一区二区| 少妇邻居内射在线,内射口| a级毛片无码视频AAAA流出91| 欧亚精品卡一卡二卡三不卡中文视频| 97色在线观看| 精品国产乱子伦一区二区三区,精品一区| 中文字幕免费高清视频HD| 精品国产综合成人亚洲区_欧美综合区 | 国产一级做a爰片在线看免费,国产一区二 |